Total Anomalous Pulmonary Venous Connection (TAPVC) with Severe Pulmonary Hypertension
نویسنده
چکیده
Here we are reporting echocardiographic findings of 8 month child with Total Anomalous Pulmonary Venous Connection (TAPVC). All pulmonary veins are draining into a venous chamber (venous confluence) posterior to Left Atrium (LA). This chamber is draining in to persistent left superior vena cava (supradiaphragmatic type) with moderate (TR) and estimated (RV) systolic pressure was 88.2 mm of Hg suggestive of severe pulmonary hypertension.
منابع مشابه
Midterm results after surgical correction of total anomalous pulmonary venous connection
Abstract Objective: To evaluate the surgical treatment of total anomalous pulmonary venous connection (TAPVC) and determination of predictors for postoperative death. Methods: Between 1995 and 2005, 80 patients aged from 1 month to 12 years underwent surgical repair for supracardiac (39), cardiac (34), infracardiac (3) or mixed (4) type of TAPVC. Systemic pulmonary hypertension (PH) in ...
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In total anomalous pulmonary venous connection (TAPVC), pulmonary venous blood flow abnormally returns to join the systemic venous tributary or right atrium, and the pulmonary vascular resistance may be elevated if a form of obstruction occurs in this circuit (1). Neonates and infants with obstructed TAPVC can present with severe cyanosis, pulmonary hypertension, and low cardiac output, requiri...
متن کاملComputed tomography features of supracardiac total anomalous pulmonary venous connection in an infant
Total anomalous pulmonary venous connection (TAPVC) is a rare congenital anomaly of the pulmonary veins drainage. In this entity, the pulmonary veins, instead of draining to left atrium, connect abnormally to the systemic venous circulation. A right-to-left shunt is obligatory for survival. Based on its type and degree of pulmonary venous obstruction, TAPVC may result in pulmonary hypertension ...
متن کاملDual pathology causing severe pulmonary hypertension following surgical repair of total anomalous pulmonary venous connection: Successful outcome following serial transcatheter interventions
Surgical repair of total anomalous pulmonary venous connection (TAPVC) can be complicated by the development of pulmonary venous stenosis later on. In addition, the vertical vein, if left unligated, can remain patent and lead to hemodynamically significant left to right shunting. We report an infant who required transcatheter correction of both these problems after surgical repair of TAPVC.
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Total anomalous pulmonary venous connection (TAPVC) is an anomaly in which the pulmonary veins are directly connected to one of the systemic veins or drain into the right atrium. Management of pulmonary hypertension after the total correction of this congenital cardiac anomaly is very important. Unligation of the vertical vein in the supracardiac type of this anomaly can be a draining pathway f...
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تاریخ انتشار 2015